|
|
NAD+ + L-carnitine <=> 3-dehydrocarnitine + NADH + H+
|
1.1.1.108
carnitine 3-dehydrogenase
1.1.1.254
(S)-carnitine 3-dehydrogenase
|
–
–
|
BM
|
|
BRENDA:
BR29174;
BS369941
KEGG:
R02395
MetaCyc:
CARNITINE-3-DEHYDROGENASE-RXN
SABIO-RK:
1975
|
|
|
|
H2O + L-Carnitine_amide <=> L-carnitine + NH3
|
3.5.1.73
carnitinamidase
|
–
|
|
|
BRENDA:
BR29515
KEGG:
R01922
MetaCyc:
CARNITINAMIDASE-RXN
|
|
|
|
H+ + L-carnitine <=> CO2 + beta-Methylcholine
|
4.1.1.42
carnitine decarboxylase
|
–
|
|
|
BRENDA:
BR302
KEGG:
R02398
MetaCyc:
CARNITINE-DECARBOXYLASE-RXN
|
|
|
|
gamma-butyrobetaine + 2-oxoglutarate + O2 <=> L-carnitine + succinate + CO2
|
1.14.11.1
gamma-butyrobetaine dioxygenase
|
–
|
MK
|
|
BRENDA:
BR40459
KEGG:
R02397
MetaCyc:
1.14.11.1-RXN
SABIO-RK:
2337;
6990
|
|
|
|
octanoyl-CoA + L-carnitine <=> Octanoyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.7
carnitine O-acetyltransferase
|
–
–
|
|
|
BRENDA:
BR43997
KEGG:
R03779
MetaCyc:
CARNITINE-O-OCTANOYLTRANSFERASE-RXN
SABIO-RK:
3538
|
|
|
|
palmitoyl-CoA + L-carnitine <=> O-palmitoyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.21
carnitine O-palmitoyltransferase
2.3.1.7
carnitine O-acetyltransferase
|
–
–
–
|
K
|
|
BRENDA:
BR44020;
BS320669;
BS435704
KEGG:
R01923
MetaCyc:
CARNITINE-O-PALMITOYLTRANSFERASE-RXN
SABIO-RK:
1977
|
|
|
|
L-carnitine + acetyl-CoA <=> acetylcarnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.21
carnitine O-palmitoyltransferase
2.3.1.6
choline O-acetyltransferase
2.3.1.7
carnitine O-acetyltransferase
|
–
–
–
–
|
|
|
BRENDA:
BR44071;
BS320451;
BS321221;
BS451962
KEGG:
R02396
MetaCyc:
CARNITINE-O-ACETYLTRANSFERASE-RXN
SABIO-RK:
10182;
420
|
|
|
|
(E)-4-(trimethylammonio)but-2-enoyl-CoA + L-carnitine <=> crotonobetaine + L-carnitinyl-CoA
|
2.8.3.21
L-carnitine CoA-transferase
|
–
|
|
|
BRENDA:
BR50971
KEGG:
R10643
MetaCyc:
RXN-14936
|
|
|
|
gamma-butyrobetainyl-CoA + L-carnitine <=> gamma-butyrobetaine + L-carnitinyl-CoA
|
2.8.3.21
L-carnitine CoA-transferase
|
–
|
BM
|
|
BRENDA:
BR50972
KEGG:
R10644
MetaCyc:
RXN0-3601
|
|
|
|
CoA + L-carnitine + ATP <=> L-carnitinyl-CoA + AMP + diphosphate
|
6.2.1.48
carnitine---CoA ligase
|
–
|
BM
|
|
BRENDA:
BR51632
KEGG:
R11632
MetaCyc:
LCARNCOALIG-RXN
|
|
|
|
L-carnitine + O2 + NADPH + H+ <=> (3R)-3-hydroxy-4-oxobutanoate + trimethylamine + NADP+ + H2O
|
1.14.13.239
carnitine monooxygenase
|
–
|
M
|
|
BRENDA:
BR52273
KEGG:
R11911
MetaCyc:
RXN-5921
|
|
|
|
L-carnitine + O2 + NADH + H+ <=> (3R)-3-hydroxy-4-oxobutanoate + trimethylamine + NAD+ + H2O
|
1.14.13.239
carnitine monooxygenase
|
–
|
|
|
BRENDA:
BR52273-a
KEGG:
R11875
MetaCyc:
RXN-5921_WOP
|
|
|
|
butyryl-CoA + L-carnitine <=> butyryl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.21
carnitine O-palmitoyltransferase
2.3.1.7
carnitine O-acetyltransferase
|
–
–
–
|
|
|
BRENDA:
BS320457
MetaCyc:
RXN-18368
|
|
|
|
myristoyl-CoA + L-carnitine <=> myristoyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.21
carnitine O-palmitoyltransferase
|
–
–
|
|
|
BRENDA:
BS320459
MetaCyc:
RXN-18370
|
|
|
|
hexanoyl-CoA + L-carnitine <=> (3R)-3-(hexanoyloxy)-4-(trimethylammonio)butanoate + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.21
carnitine O-palmitoyltransferase
2.3.1.7
carnitine O-acetyltransferase
|
–
–
–
|
|
|
BRENDA:
BS320463;
BS451963
MetaCyc:
RXN-18369
|
|
|
|
decanoyl-CoA + L-carnitine <=> L-decanoyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.21
carnitine O-palmitoyltransferase
2.3.1.7
carnitine O-acetyltransferase
|
–
–
–
|
|
|
BRENDA:
BS320467
MetaCyc:
RXN-18371
SABIO-RK:
6694
|
|
|
|
lauroyl-CoA + L-carnitine <=> lauroyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.21
carnitine O-palmitoyltransferase
|
–
–
|
|
|
BRENDA:
BS320469
MetaCyc:
RXN-18373
|
|
|
|
stearoyl-CoA + L-carnitine <=> O-fatty-acyl-L-carnitine + CoA
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
|
|
BRENDA:
BS320676
MetaCyc:
RXN-18372
|
|
|
|
acyl-L-carnitine + H2O <=> L-carnitine + fatty_acid
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS64352
KEGG:
R01924
|
|
|
|
propionyl-CoA + L-carnitine <=> propionylcarnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.7
carnitine O-acetyltransferase
|
–
–
|
|
|
BRENDA:
BS321225
MetaCyc:
RXN-18367
SABIO-RK:
10184
|
|
|
|
butyryl-CoA + L-carnitine <=> CoA + butyrylcarnitine
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
BRENDA:
BS435374
SABIO-RK:
6699
|
|
|
|
Octanoyl-L-carnitine + H2O <=> Octanoate + L-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS64353
SABIO-RK:
10178
|
|
|
|
lauroyl-L-carnitine + H2O <=> laurate + L-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS64355
SABIO-RK:
10179
|
|
|
|
myristoyl-L-carnitine + H2O <=> myristic_acid + L-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS64356
SABIO-RK:
10187
|
|
|
|
O-(long-chain-acyl)-L-carnitine + H2O <=> L-carnitine + fatty_acid + H+
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
MetaCyc:
ACYLCARNITINE-HYDROLASE-RXN
|
|
|
|
D-carnitine <=> L-carnitine
|
5.1.2.M1
|
–
|
M
|
|
MetaCyc:
CARNRACE-RXN
|
|
|
|
O-medium-chain-acyl-L-carnitine + H2O <=> L-carnitine + medium_chain_fatty_acid + H+
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
MetaCyc:
RXN-18548
|
|
|
|
L-carnitine + hydroxyacetyl-CoA <=> O-glycolyl-L-carnitine + CoA
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
MetaCyc:
RXN-21226
|
|
|
|
O-(long-chain-acyl)-L-carnitine + CoA <=> stearoyl-CoA + L-carnitine
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
M
|
|
MetaCyc:
RXN-21778
|
|
|
|
stearoyl-CoA + L-carnitine <=> O-(long-chain-acyl)-L-carnitine + CoA
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
M
|
|
MetaCyc:
RXN-9918
|
|
|
|
gamma-butyrobetaine + L-carnitine <=> gamma-butyrobetaine + L-carnitine
|
not assigned
|
–
|
|
|
MetaCyc:
TRANS-RXN-100
|
|
|
|
O-(long-chain-acyl)-L-carnitine + L-carnitine <=> O-(long-chain-acyl)-L-carnitine + L-carnitine
|
not assigned
|
–
|
M
|
|
MetaCyc:
TRANS-RXN-177
|
|
|
|
palmitoyl-L-carnitine + CoA <=> palmitoyl-CoA + L-carnitine
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320474
|
|
|
|
acetoacetyl-CoA + L-carnitine <=> acetoacetyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320453
|
|
|
|
O-acetoacetyl(-)carnitine + CoA <=> acetoacetyl-CoA + L-carnitine
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
BRENDA:
BS321223
|
|
|
|
L-carnitine + 2-oxoglutarate + O2 <=> 3-dehydrocarnitine + succinate + CO2
|
1.14.11.1
gamma-butyrobetaine dioxygenase
|
–
|
|
|
BRENDA:
BS443674
|
|
|
|
butyryl-CoA + L-carnitine <=> CoA + O-butyryl-L-carnitine
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
BRENDA:
BS451964
|
|
|
|
oleoyl-CoA + L-carnitine <=> CoA + L-oleoylcarnitine
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
|
|
BRENDA:
BS320680
|
|
|
|
bromoacetyl-CoA + L-carnitine <=> bromoacetylcarnitine + CoA
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
BRENDA:
BS321244
|
|
|
|
arachidoyl-CoA + L-carnitine <=> CoA + L-arachidoylcarnitine
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
|
|
BRENDA:
BS320677
|
|
|
|
4,8-dimethylnonanoyl-CoA + L-carnitine <=> 4,8-dimethylnonanoyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.21
carnitine O-palmitoyltransferase
|
–
–
|
|
|
BRENDA:
BS320485
|
|
|
|
propionyl-CoA + L-carnitine <=> propionyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320455
|
|
|
|
propionyl-CoA + L-carnitine <=> CoA + O-propionyl-L-carnitine
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
BRENDA:
BS451965
|
|
|
|
heptanoyl-L-carnitine + CoA <=> heptanoyl-CoA + L-carnitine
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320466
|
|
|
|
heptanoyl-CoA + L-carnitine <=> L-heptanoyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320465
|
|
|
|
3-methylglutaryl-CoA + L-carnitine <=> 3-methylglutaryl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320481
|
|
|
|
octanoyl-CoA + L-carnitine <=> CoA + octanoylcarnitine
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
BRENDA:
BS435674
|
|
|
|
3-keto-4-pentenoyl-CoA + L-carnitine <=> 3-keto-4-pentenoylcarnitine + CoA
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
BRENDA:
BS321243
|
|
|
|
pivaloyl-L-carnitine + CoA <=> pivaloyl-CoA + L-carnitine
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320480
|
|
|
|
pivaloyl-CoA + L-carnitine <=> L-pivaloyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320479
|
|
|
|
erucoyl-CoA + L-carnitine <=> CoA + L-erucoylcarnitine
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
|
|
BRENDA:
BS320679
|
|
|
|
acyl-CoA + L-carnitine <=> acyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
2.3.1.21
carnitine O-palmitoyltransferase
2.3.1.7
carnitine O-acetyltransferase
|
–
–
–
|
B
|
|
BRENDA:
BS320449
|
|
|
|
palmitoyl-L-carnitine + H2O <=> palmitate + L-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS64360
|
|
|
|
Decanoyl-L-carnitine + CoA <=> decanoyl-CoA + L-carnitine
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320468
|
|
|
|
trans-2-hexadecenoyl-CoA + L-carnitine <=> CoA + trans-2-hexadecenoyl-L-carnitine
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
|
|
BRENDA:
BS421582
|
|
|
|
valproyl-CoA + L-carnitine <=> L-valproyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320477
|
|
|
|
docosanhexaenoyl-CoA + L-carnitine <=> CoA + L-docosanhexaenoylcarnitine
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
|
|
BRENDA:
BS320681
|
|
|
|
linoleoyl-CoA + L-carnitine <=> CoA + L-linoleoylcarnitine
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
|
|
BRENDA:
BS320678
|
|
|
|
3-hydroxy-3-methylglutaryl-CoA + L-carnitine <=> 3-hydroxy-3-methylglutaryl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320483
|
|
|
|
beta-hydroxy-beta-methylglutaryl-L-carnitine + CoA <=> 3-hydroxy-3-methylglutaryl-CoA + L-carnitine
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320484
|
|
|
|
palmitoleoyl-CoA + L-carnitine <=> CoA + L-palmitoleoylcarnitine
|
2.3.1.21
carnitine O-palmitoyltransferase
|
–
|
|
|
BRENDA:
BS421162
|
|
|
|
O-fatty-acyl-L-carnitine + H2O <=> fatty_acid + L-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BR10651
|
|
|
|
butyryl-L-carnitine + H2O <=> Butyrate + L-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS430012
|
|
|
|
2 palmitoylcarnitine + 2 H2O <=> 2 palmitate + L-carnitine + D-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS364053
|
|
|
|
acetylcarnitine + H2O <=> acetate + L-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS364052
|
|
|
|
L-carnitine + 2-oxoglutarate + Ozone <=> 3-dehydrocarnitine + succinate + HCO3-
|
1.14.11.1
gamma-butyrobetaine dioxygenase
|
–
|
|
|
BRENDA:
BS451243
|
|
|
|
malonyl-CoA + L-carnitine <=> malonyl-L-carnitine + CoA
|
2.3.1.137
carnitine O-octanoyltransferase
|
–
|
|
|
BRENDA:
BS320461
|
|
|
|
malonylcarnitine + CoA <=> malonyl-CoA + L-carnitine
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
BRENDA:
BS321237
|
|
|
|
Decanoyl-L-carnitine + H2O <=> Decanoate + L-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS64354
|
|
|
|
acetyl-L-(-)-carnitine + H2O <=> acetate + L-carnitine
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
BRENDA:
BS429868
|
|
|
|
O2 + gamma-butyrobetaine + 3-Bromo-2-ketoglutarate <=> 3-Bromo-succinate + L-carnitine + CO2
|
1.14.11.1
gamma-butyrobetaine dioxygenase
|
–
|
|
|
SABIO-RK:
6991
|
|
|
|
myristoyl-CoA + L-carnitine <=> CoA + O-Myristoylcarnitine
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
SABIO-RK:
6690
|
|
|
|
hexanoyl-CoA + L-carnitine <=> hexanoylcarnitine + CoA
|
2.3.1.7
carnitine O-acetyltransferase
|
–
|
|
|
SABIO-RK:
6692
|
|
|
|
H2O + L-palmitoylcarnitine <=> L-carnitine + palmitate
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
SABIO-RK:
10185
|
|
|
|
decanoylcarnitine + H2O <=> L-carnitine + Decanoate
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
SABIO-RK:
10192
|
|
|
|
H2O + L-decanoyl-L-carnitine <=> L-carnitine + Decanoate
|
3.1.1.28
acylcarnitine hydrolase
|
–
|
|
|
SABIO-RK:
10190
|
|